Total sequestration of the right lung.

A 2-day-old baby with severe respiratory distress and cyanosis was admitted to the hospital with a totally opacified right pleural cavity. Preoperative studies demonstrated absence of the right pulmonary artery, and a patent ductus arteriosus, and a left pulmonary artery pressure of 85/45 mm. Hg. The hypoplastic right lung received its entire blood supply from multiple vessels through the diaphragm. The infant's condition improved initially after a right pneumonectomy, but she died of progressive respiratory insufficiency at the age of 7 months.