Literature DB >> 11051765

Molecular and cell biology of acid beta-glucosidase and prosaposin.

X Qi1, G A Grabowski.   

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Year:  2001        PMID： 11051765     DOI： 10.1016/s0079-6603(00)66030-0

Source DB:  PubMed          Journal:  Prog Nucleic Acid Res Mol Biol        ISSN： 0079-6603


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  18 in total

1.  Lipids regulate the hydrolysis of membrane bound glucosylceramide by lysosomal β-glucocerebrosidase.

Authors:  Misbaudeen Abdul-Hammed; Bernadette Breiden; Günter Schwarzmann; Konrad Sandhoff
Journal:  J Lipid Res       Date:  2017-01-26       Impact factor: 5.922

2.  A mutation within the saposin D domain in a Gaucher disease patient with normal glucocerebrosidase activity.

Authors:  Anna Diaz-Font; Bru Cormand; Raül Santamaria; Lluïsa Vilageliu; Daniel Grinberg; Amparo Chabás
Journal:  Hum Genet       Date:  2005-04-23       Impact factor: 4.132

3.  The interaction between progranulin and prosaposin is mediated by granulins and the linker region between saposin B and C.

Authors:  Xiaolai Zhou; Peter M Sullivan; Lirong Sun; Fenghua Hu
Journal:  J Neurochem       Date:  2017-08-04       Impact factor: 5.372

4.  Phospholipid membrane interactions of saposin C: in situ atomic force microscopic study.

Authors:  Hong Xing You; Xiaoyang Qi; Gregory A Grabowski; Lei Yu
Journal:  Biophys J       Date:  2003-03       Impact factor: 4.033

5.  Purified recombinant human prosaposin forms oligomers that bind procathepsin D and affect its autoactivation.

Authors:  Madanan Madathiparambil Gopalakrishnan; Hans-Wilhelm Grosch; Silvia Locatelli-Hoops; Norbert Werth; Eva Smolenová; Michael Nettersheim; Konrad Sandhoff; Andrej Hasilik
Journal:  Biochem J       Date:  2004-11-01       Impact factor: 3.857

6.  Bone events and evolution of biologic markers in Gaucher disease before and during treatment.

Authors:  Jérôme Stirnemann; Nadia Belmatoug; Corine Vincent; Olivier Fain; Bruno Fantin; France Mentré
Journal:  Arthritis Res Ther       Date:  2010-08-09       Impact factor: 5.156

7.  Prosaposin facilitates sortilin-independent lysosomal trafficking of progranulin.

Authors:  Xiaolai Zhou; Lirong Sun; Francisco Bastos de Oliveira; Xiaoyang Qi; William J Brown; Marcus B Smolka; Ying Sun; Fenghua Hu
Journal:  J Cell Biol       Date:  2015-09-14       Impact factor: 10.539

8.  Neuronopathic Gaucher disease in the mouse: viable combined selective saposin C deficiency and mutant glucocerebrosidase (V394L) mice with glucosylsphingosine and glucosylceramide accumulation and progressive neurological deficits.

Authors:  Ying Sun; Benjamin Liou; Huimin Ran; Matthew R Skelton; Michael T Williams; Charles V Vorhees; Kazuyuki Kitatani; Yusuf A Hannun; David P Witte; You-Hai Xu; Gregory A Grabowski
Journal:  Hum Mol Genet       Date:  2010-01-04       Impact factor: 6.150

9.  Specific saposin C deficiency: CNS impairment and acid beta-glucosidase effects in the mouse.

Authors:  Ying Sun; Huimin Ran; Matt Zamzow; Kazuyuki Kitatani; Matthew R Skelton; Michael T Williams; Charles V Vorhees; David P Witte; Yusuf A Hannun; Gregory A Grabowski
Journal:  Hum Mol Genet       Date:  2009-12-16       Impact factor: 6.150

10.  The French Gaucher's disease registry: clinical characteristics, complications and treatment of 562 patients.

Authors:  Jérôme Stirnemann; Marie Vigan; Dalil Hamroun; Djazia Heraoui; Linda Rossi-Semerano; Marc G Berger; Christian Rose; Fabrice Camou; Christine de Roux-Serratrice; Bernard Grosbois; Pierre Kaminsky; Alain Robert; Catherine Caillaud; Roselyne Froissart; Thierry Levade; Agathe Masseau; Cyril Mignot; Frédéric Sedel; Dries Dobbelaere; Marie T Vanier; Vassili Valayanopoulos; Olivier Fain; Bruno Fantin; Thierry Billette de Villemeur; France Mentré; Nadia Belmatoug
Journal:  Orphanet J Rare Dis       Date:  2012-10-09       Impact factor: 4.123
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