Literature DB >> 10969696

Bilateral sequential lung transplant for ectodermal dysplasia.

W R Smythe1, N D Bridges, J W Gaynor, S Nicolson, B J Clark, T L Spray.   

Abstract

A case of bilateral sequential lung transplantation for anhidrotic ectodermal dysplasia is presented. The patient was a 16-year-old male with end-stage lung disease secondary to chronic severe respiratory infection. Although a relatively rare disease, the common association of fatal pulmonary compromise in those affected with this disorder warrants consideration of lung transplantation as a viable therapeutic option.

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Year:  2000        PMID: 10969696     DOI: 10.1016/s0003-4975(00)01571-x

Source DB:  PubMed          Journal:  Ann Thorac Surg        ISSN: 0003-4975            Impact factor:   4.330


  3 in total

1.  Glandular gene expression of sinus mucosa in chronic rhinosinusitis with and without cystic fibrosis.

Authors:  Xiaofang Wu; Jennifer R Peters-Hall; Svetlana Ghimbovschi; Remy Mimms; Mary C Rose; Maria T Peña
Journal:  Am J Respir Cell Mol Biol       Date:  2010-12-22       Impact factor: 6.914

2.  A novel X-linked disorder of immune deficiency and hypohidrotic ectodermal dysplasia is allelic to incontinentia pigmenti and due to mutations in IKK-gamma (NEMO).

Authors:  J Zonana; M E Elder; L C Schneider; S J Orlow; C Moss; M Golabi; S K Shapira; P A Farndon; D W Wara; S A Emmal; B M Ferguson
Journal:  Am J Hum Genet       Date:  2000-10-24       Impact factor: 11.025

3.  Myd88 deficiency influences murine tracheal epithelial metaplasia and submucosal gland abundance.

Authors:  Adam Giangreco; Liwen Lu; Dawn J Mazzatti; Bradley Spencer-Dene; Emma Nye; Vitor Hugo Teixeira; Sam M Janes
Journal:  J Pathol       Date:  2011-06       Impact factor: 7.996

  3 in total

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