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7 in total

1. Tightly bound nucleotides of the energy-transducing ATPase of chloroplasts and their role in photophosphorylation.

Authors: D A Harris; E D Slater
Journal: Biochim Biophys Acta Date: 1975-05-15

2. Guanidinoacetate methyltransferase deficiency: the first inborn error of creatine metabolism in man.

Authors: S Stöckler; D Isbrandt; F Hanefeld; B Schmidt; K von Figura
Journal: Am J Hum Genet Date: 1996-05 Impact factor: 11.025

3. The calcium-binding ATPase inhibitor protein from bovine heart mitochondria. Purification and properties.

Authors: E W Yamada; N J Huzel
Journal: J Biol Chem Date: 1988-08-15 Impact factor: 5.157

4. The binding and release of the inhibitor protein are governed independently by ATP and membrane potential in ox-heart submitochondrial vesicles.

Authors: G Lippe; M C Sorgato; D A Harris
Journal: Biochim Biophys Acta Date: 1988-03-30

5. Anomalies of mitochondrial ATP synthase regulation in four different types of neuronal ceroid lipofuscinosis.

Authors: A M Das; R D Jolly; A Kohlschütter
Journal: Mol Genet Metab Date: 1999-04 Impact factor: 4.797

6. Differential effects of creatine depletion on the regulation of enzyme activities and on creatine-stimulated mitochondrial respiration in skeletal muscle, heart, and brain.

Authors: E O'Gorman; G Beutner; T Wallimann; D Brdiczka
Journal: Biochim Biophys Acta Date: 1996-09-12

7. ATP synthesis kinetic properties of mitochondria isolated from the rat extensor digitorum longus muscle depleted of creatine with beta-guanidinopropionic acid.

Authors: D Freyssenet; P Berthon; A Geyssant; C Denis
Journal: Biochim Biophys Acta Date: 1994-07-29

7 in total

3 in total

1. X-linked creatine transporter defect: a report on two unrelated boys with a severe clinical phenotype.

Authors: I A Anselm; I M Anselm; F S Alkuraya; G S Salomons; C Jakobs; A B Fulton; M Mazumdar; M Rivkin; R Frye; T Young Poussaint; D Marsden
Journal: J Inherit Metab Dis Date: 2006-02 Impact factor: 4.982

2. Presence of normal creatine in the muscle of a patient with a mutation in the creatine transporter: a case study.

Authors: Gail J Pyne-Geithman; Ton J deGrauw; Kim M Cecil; Gail Chuck; Melissa A Lyons; Yukisato Ishida; Joseph F Clark
Journal: Mol Cell Biochem Date: 2004-07 Impact factor: 3.396

3. Disturbed energy metabolism and muscular dystrophy caused by pure creatine deficiency are reversible by creatine intake.

Authors: C I Nabuurs; C U Choe; A Veltien; H E Kan; L J C van Loon; R J T Rodenburg; J Matschke; B Wieringa; G J Kemp; D Isbrandt; A Heerschap
Journal: J Physiol Date: 2012-11-05 Impact factor: 5.182

3 in total