Literature DB >> 10896293

Methylmalonic acid induces excitotoxic neuronal damage in vitro.

S Kölker1, B Ahlemeyer, J Krieglstein, G F Hoffmann.   

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Year:  2000        PMID： 10896293     DOI： 10.1023/a:1005631230455

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN： 0141-8955            Impact factor:   4.982


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  5 in total

1.  3-Hydroxyglutaric and glutaric acids are neurotoxic through NMDA receptors in vitro.

Authors:  S Kölker; B Ahlemeyer; J Krieglstein; G F Hoffmann
Journal:  J Inherit Metab Dis       Date:  1999-05       Impact factor: 4.982

2.  Morphological and biochemical maturation of neurones cultured in the absence of glial cells.

Authors:  B Pettmann; J C Louis; M Sensenbrenner
Journal:  Nature       Date:  1979-10-04       Impact factor: 49.962

Review 3.  Bioenergetics and glutamate excitotoxicity.

Authors:  J G Greene; J T Greenamyre
Journal:  Prog Neurobiol       Date:  1996-04       Impact factor: 11.685

Review 4.  Neurological dysfunction in methylmalonic acidaemia is probably related to the inhibitory effect of methylmalonate on brain energy production.

Authors:  M Wajner; J C Coelho
Journal:  J Inherit Metab Dis       Date:  1997-11       Impact factor: 4.982

5.  CT and MR of the brain in the diagnosis of organic acidemias. Experiences from 107 patients.

Authors:  J Brismar; P T Ozand
Journal:  Brain Dev       Date:  1994-11       Impact factor: 1.961
  5 in total
  7 in total

Review 1.  Age-related lysosomal dysfunction: an unrecognized roadblock for cobalamin trafficking?

Authors:  Hua Zhao; Ulf T Brunk; Brett Garner
Journal:  Cell Mol Life Sci       Date:  2011-10-21       Impact factor: 9.261

2.  Experimental evidence that methylmalonic acid provokes oxidative damage and compromises antioxidant defenses in nerve terminal and striatum of young rats.

Authors:  Carolina Gonçalves Fernandes; Clarissa Günther Borges; Bianca Seminotti; Alexandre Umpierrez Amaral; Lisiane Aurélio Knebel; Paula Eichler; Anderson Büker de Oliveira; Guilhian Leipnitz; Moacir Wajner
Journal:  Cell Mol Neurobiol       Date:  2011-03-22       Impact factor: 5.046

3.  Methylmalonic Acid Impairs Cell Respiration and Glutamate Uptake in C6 Rat Glioma Cells: Implications for Methylmalonic Acidemia.

Authors:  Renata T Costa; Marcella B Santos; Carlos Alberto-Silva; Daniel C Carrettiero; César A J Ribeiro
Journal:  Cell Mol Neurobiol       Date:  2022-06-08       Impact factor: 5.046

Review 4.  The Regulation and Characterization of Mitochondrial-Derived Methylmalonic Acid in Mitochondrial Dysfunction and Oxidative Stress: From Basic Research to Clinical Practice.

Authors:  Yige Liu; Shanjie Wang; Xiaoyuan Zhang; Hengxuan Cai; Jinxin Liu; Shaohong Fang; Bo Yu
Journal:  Oxid Med Cell Longev       Date:  2022-05-24       Impact factor: 7.310

5.  Diffusion-weighted imaging in the assessment of neurological damage in patients with methylmalonic aciduria.

Authors:  A P Burlina; R Manara; M Calderone; S Catuogno; A B Burlina
Journal:  J Inherit Metab Dis       Date:  2003       Impact factor: 4.982

6.  Higher Vulnerability of Menadione-Exposed Cortical Astrocytes of Glutaryl-CoA Dehydrogenase Deficient Mice to Oxidative Stress, Mitochondrial Dysfunction, and Cell Death: Implications for the Neurodegeneration in Glutaric Aciduria Type I.

Authors:  Marília Danyelle Nunes Rodrigues; Bianca Seminotti; Ângela Zanatta; Aline de Mello Gonçalves; Bruna Bellaver; Alexandre Umpierrez Amaral; André Quincozes-Santos; Stephen Irwin Goodman; Michael Woontner; Diogo Onofre Souza; Moacir Wajner
Journal:  Mol Neurobiol       Date:  2016-08-10       Impact factor: 5.590

7.  Disorders of branched chain amino acid metabolism.

Authors:  I Manoli; C P Venditti
Journal:  Transl Sci Rare Dis       Date:  2016-11-07
  7 in total

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