[Atypical retinopathia pigmentosa with central retinoschisis (Goldmann-Favre) (author's transl)].

A family is presented whose two daughters suffer from Goldmann-Favre disease. They have a retinoschisis and bone corpuscle like pigmentations. Both the girls have pathological ERG's (reduced b-waves, potentials up to 40 muV, no a-waves). The EOG of the younger is normal (Arden ratio 200%), but the EOG of the elder sister is pathological (Arden ratio right 120%, left 150%).