Single right ventricle (double-inlet right ventricle). A pathological specimen with comments on embryology.

This paper describes a pathological specimen of double-inlet right ventricle in which no remains of a hypoplastic left ventricle were found. An ontogenetic explanation of the malformation is presented based on the development of the normal human embryos. This case may be an example of exaggerated displacement of the atrioventricular canal towards the bulbus cordis in which the left ventricular cavity is extremely hypoplastic or aplastic and is not recognizable. The concept of early and late displacement is introduced.