Literature DB >> 10712426

The missing link in lysosomal enzyme targeting.

W S Sly1.   

Abstract

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Year:  2000        PMID： 10712426      PMCID： PMC292458          DOI： 10.1172/JCI9479

Source DB:  PubMed          Journal:  J Clin Invest        ISSN： 0021-9738            Impact factor:   14.808


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  18 in total

1.  Lysosomal enzyme phosphorylation. I. Protein recognition determinants in both lobes of procathepsin D mediate its interaction with UDP-GlcNAc:lysosomal enzyme N-acetylglucosamine-1-phosphotransferase.

Authors:  T J Baranski; A B Cantor; S Kornfeld
Journal:  J Biol Chem       Date:  1992-11-15       Impact factor: 5.157

Review 2.  Lysosomal enzymes and their receptors.

Authors:  K von Figura; A Hasilik
Journal:  Annu Rev Biochem       Date:  1986       Impact factor: 23.643

3.  A recognition marker required for uptake of a lysosomal enzyme by cultured fibroblasts.

Authors:  S Hickman; L J Shapiro; E F Neufeld
Journal:  Biochem Biophys Res Commun       Date:  1974-03-15       Impact factor: 3.575

4.  Clinical, biochemical, and ultrastructural studies in a case of chondrodystrophy presenting the I-cell phenotype in tissue culture.

Authors:  M Tondeur; E Vamos-Hurwitz; S Mockel-Pohl; J P Dereume; N Cremer; H Loeb
Journal:  J Pediatr       Date:  1971-09       Impact factor: 4.406

5.  I-cell disease: multiple lysosomal-enzyme defect.

Authors:  J Lightbody; U Wiesmann; B Hadorn; N Herschkowitz
Journal:  Lancet       Date:  1971-02-27       Impact factor: 79.321

6.  Genetic heterogeneity in multiple lysosomal hydrolase deficiency.

Authors:  J H Glaser; W H McAlister; W S Sly
Journal:  J Pediatr       Date:  1974-08       Impact factor: 4.406

Review 7.  Trafficking of lysosomal enzymes.

Authors:  S Kornfeld
Journal:  FASEB J       Date:  1987-12       Impact factor: 5.191

8.  Purification and multimeric structure of bovine N-acetylglucosamine-1-phosphodiester alpha-N-acetylglucosaminidase.

Authors:  R Kornfeld; M Bao; K Brewer; C Noll; W M Canfield
Journal:  J Biol Chem       Date:  1998-09-04       Impact factor: 5.157

9.  Mucolipidosis III (pseudo-Hurler polydystrophy): Clinical and laboratory studies in a series of 12 patients.

Authors:  T E Kelly; G H Thomas; H A Taylor; V A McKusick; W S Sly; J H Glaser; M Robinow; L Luzzatti; C Espiritu; M Feingold; M J Bull; E M Ashenhurst; E J Ives
Journal:  Johns Hopkins Med J       Date:  1975-10

10.  Mutant enzymatic and cytological phenotypes in cultured human fibroblasts.

Authors:  J G Leroy; R I Demars
Journal:  Science       Date:  1967-08-18       Impact factor: 47.728
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  3 in total

1.  Early initiation of enzyme replacement therapy improves metabolic correction in the brain tissue of aspartylglycosaminuria mice.

Authors:  Ulla Dunder; Pirjo Valtonen; Eira Kelo; Ilkka Mononen
Journal:  J Inherit Metab Dis       Date:  2010-07-06       Impact factor: 4.982

2.  Abnormal expressions of the subunits of the UDP-N-acetylglucosamine: lysosomal enzyme, N-acetylglucosamine-1-phosphotransferase, result in the formation of cytoplasmic vacuoles resembling those of the I-cells.

Authors:  Cecilia Y S Ho; Nelson L S Tang; Ava K Y Yeung; Abby K C Lau; Joannie Hui; Anthony W I Lo
Journal:  J Mol Med (Berl)       Date:  2006-12-08       Impact factor: 4.599

Review 3.  Sweet complementarity: the functional pairing of glycans with lectins.

Authors:  H-J Gabius; J C Manning; J Kopitz; S André; H Kaltner
Journal:  Cell Mol Life Sci       Date:  2016-03-08       Impact factor: 9.261
  3 in total

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