Total aortic replacement for aortitis syndrome: report of a case.

We report herein the case of a 35-year-old woman who was administered steroid therapy based on a diagnosis of aortitis syndrome. Despite this treatment, the symptoms of cardiac failure gradually progressed, and she was referred to our hospital to undergo surgery. Preoperative evaluations revealed a large aneurysm extending from the ascending aorta to the thoracoabdominal aorta. A two-staged total aortic replacement was carried out and postoperative digital subtraction angiography showed excellent reconstruction of the entire aorta.