Literature DB >> 10493778

Identification of a missense mutation in the alphaA-crystallin gene of the lop18 mouse.

B Chang1, N L Hawes, T H Roderick, R S Smith, J R Heckenlively, J Horwitz, M T Davisson.   

Abstract

PURPOSE: The mouse lop18 (lens opacity 18) mutation causes a white cataract obvious at weaning age. It soon progresses to a large white nuclear cataract with mild cortical changes. The mutation maps to mouse Chromosome 17 in close linkage to the alphaA-crystallin (Crya) gene, which encodes one of the major vertebrate eye lens proteins. Here we report the identification of a missense mutation in the alphaA-crystallin gene of lop18/lop18 mutant mice.
METHODS: PCR primers were designed based on the alphaA-crystallin gene sequence from GenBank and PCR products were sequenced.
RESULTS: We have analysed the sequence of the alphaA-crystallin gene from the lop18/lop18 mouse and identified a missense mutation. This mutation is tightly associated with the cataract phenotype, as no recombination was detected in 112 meioses.
CONCLUSIONS: Our results suggest that a missense mutation in the alphaA-crystallin gene is responsible for the lop18/lop18 phenotype and Cryalop18 should be used as a gene symbol for the lop18 mutation.

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Year:  1999        PMID: 10493778

Source DB:  PubMed          Journal:  Mol Vis        ISSN: 1090-0535            Impact factor:   2.367


  13 in total

1.  Maternal germ-line transmission of mutant mtDNAs from embryonic stem cell-derived chimeric mice.

Authors:  J E Sligh; S E Levy; K G Waymire; P Allard; D L Dillehay; S Nusinowitz; J R Heckenlively; G R MacGregor; D C Wallace
Journal:  Proc Natl Acad Sci U S A       Date:  2000-12-19       Impact factor: 11.205

2.  A novel alphaB-crystallin mutation associated with autosomal dominant congenital lamellar cataract.

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Journal:  Invest Ophthalmol Vis Sci       Date:  2006-03       Impact factor: 4.799

3.  Dense cataract and microphthalmia (dcm) in BALB/c mice is caused by mutations in the GJA8 locus.

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Journal:  J Genet       Date:  2010-08       Impact factor: 1.166

4.  Congenital cataract and macular hypoplasia in humans associated with a de novo mutation in CRYAA and compound heterozygous mutations in P.

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Journal:  Graefes Arch Clin Exp Ophthalmol       Date:  2006-02-02       Impact factor: 3.117

Review 5.  The genetics of childhood cataract.

Authors:  P J Francis; V Berry; S S Bhattacharya; A T Moore
Journal:  J Med Genet       Date:  2000-07       Impact factor: 6.318

6.  Early transposable element insertion in intron 9 of the Hsf4 gene results in autosomal recessive cataracts in lop11 and ldis1 mice.

Authors:  Elijah Talamas; Lavinia Jackson; Matthew Koeberl; Todd Jackson; John L McElwee; Norman L Hawes; Bo Chang; Monica M Jablonski; D J Sidjanin
Journal:  Genomics       Date:  2006-04-03       Impact factor: 5.736

7.  Effect of trifluoroethanol on the structural and functional properties of alpha-crystallin.

Authors:  V Srinivas; P Santhoshkumar; K Krishna Sharma
Journal:  J Protein Chem       Date:  2002-02

8.  An alphaA-crystallin gene mutation, Arg12Cys, causing inherited cataract-microcornea exhibits an altered heat-shock response.

Authors:  Li-Yun Zhang; Gary Hin-Fai Yam; Pancy Oi-Sin Tam; Ricky Yiu-Kwong Lai; Dennis Shun-Chiu Lam; Chi-Pui Pang; Dorothy Shu-Ping Fan
Journal:  Mol Vis       Date:  2009-06-04       Impact factor: 2.367

Review 9.  Mouse models of cataract.

Authors:  Jochen Graw
Journal:  J Genet       Date:  2009-12       Impact factor: 1.166

10.  Structure and mechanism of protein stability sensors: chaperone activity of small heat shock proteins.

Authors:  Hassane S McHaourab; Jared A Godar; Phoebe L Stewart
Journal:  Biochemistry       Date:  2009-05-12       Impact factor: 3.162

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