Atrophy of the left lobe of the liver and anomalous hepatic vessel in a patient with Yunis-Varon syndrome.

Yunis-Varon syndrome is inherited as an autosomal recessive trait. It is characterized by facial and digit anomalies. This report describes a young woman with clinical features of this syndrome, atrophy of the left lobe of the liver, and a vascular anomaly. Liver abnormalities have not been described as features of this rare syndrome.