Literature DB >> 10459916

Pulmonary disease severity in men with deltaF508 cystic fibrosis and residual chloride secretion.

S R Thomas, A Jaffe, D M Geddes, M E Hodson, E W Alton.   

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Year:  1999        PMID： 10459916     DOI： 10.1016/S0140-6736(98)05447-6

Source DB:  PubMed          Journal:  Lancet        ISSN： 0140-6736            Impact factor:   79.321


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  11 in total

1.  COX-2: a link between airway inflammation and disordered chloride secretion in cystic fibrosis?

Authors:  A Clayton; A J Knox
Journal:  Thorax       Date:  2006-07       Impact factor: 9.139

2.  Gene expression in transformed lymphocytes reveals variation in endomembrane and HLA pathways modifying cystic fibrosis pulmonary phenotypes.

Authors:  Wanda K O'Neal; Paul Gallins; Rhonda G Pace; Hong Dang; Whitney E Wolf; Lisa C Jones; XueLiang Guo; Yi-Hui Zhou; Vered Madar; Jinyan Huang; Liming Liang; Miriam F Moffatt; Garry R Cutting; Mitchell L Drumm; Johanna M Rommens; Lisa J Strug; Wei Sun; Jaclyn R Stonebraker; Fred A Wright; Michael R Knowles
Journal:  Am J Hum Genet       Date:  2015-01-29       Impact factor: 11.025

3.  Chloride conductance and genetic background modulate the cystic fibrosis phenotype of Delta F508 homozygous twins and siblings.

Authors:  I Bronsveld; F Mekus; J Bijman; M Ballmann; H R de Jonge; U Laabs; D J Halley; H Ellemunter; G Mastella; S Thomas; H J Veeze; B Tümmler
Journal:  J Clin Invest       Date:  2001-12       Impact factor: 14.808

4.  Chloride Conductance, Nasal Potential Difference and Cystic Fibrosis Pathophysiology.

Authors:  Elenara da Fonseca Andrade Procianoy; Fernando Antônio de Abreu E Silva; Paulo José Cauduro Maróstica; Paul M Quinton
Journal:  Lung       Date:  2019-11-16       Impact factor: 2.584

5.  Nasal airway ion transport is linked to the cystic fibrosis phenotype in adult patients.

Authors:  I Fajac; D Hubert; D Guillemot; I Honoré; T Bienvenu; F Volter; J Dall'Ava-Santucci; D J Dusser
Journal:  Thorax       Date:  2004-11       Impact factor: 9.139

6.  High-content functional screen to identify proteins that correct F508del-CFTR function.

Authors:  Agata M Trzcinska-Daneluti; Diane Ly; Lise Huynh; Chong Jiang; Christopher Fladd; Daniela Rotin
Journal:  Mol Cell Proteomics       Date:  2008-12-15       Impact factor: 5.911

7.  Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770.

Authors:  Fredrick Van Goor; Sabine Hadida; Peter D J Grootenhuis; Bill Burton; Dong Cao; Tim Neuberger; Amanda Turnbull; Ashvani Singh; John Joubran; Anna Hazlewood; Jinglan Zhou; Jason McCartney; Vijayalaksmi Arumugam; Caroline Decker; Jennifer Yang; Chris Young; Eric R Olson; Jeffery J Wine; Raymond A Frizzell; Melissa Ashlock; Paul Negulescu
Journal:  Proc Natl Acad Sci U S A       Date:  2009-10-21       Impact factor: 11.205

Review 8.  Detection of cystic fibrosis transmembrane conductance regulator activity in early-phase clinical trials.

Authors:  Steven M Rowe; Frank Accurso; John P Clancy
Journal:  Proc Am Thorac Soc       Date:  2007-08-01

9.  The CFTR frameshift mutation 3905insT and its effect at transcript and protein level.

Authors:  Javier Sanz; Thomas von Känel; Mircea Schneider; Bernhard Steiner; André Schaller; Sabina Gallati
Journal:  Eur J Hum Genet       Date:  2009-09-02       Impact factor: 4.246

10.  Apical CFTR expression in human nasal epithelium correlates with lung disease in cystic fibrosis.

Authors:  Marit Arianne van Meegen; Suzanne Willemina Julia Terheggen-Lagro; Kirsten Judith Koymans; Cornelis Korstiaan van der Ent; Jeffrey Matthijn Beekman
Journal:  PLoS One       Date:  2013-03-06       Impact factor: 3.240
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