Literature DB >> 10447793

A patient with neurofibromatosis type 1 and watery diarrhoea syndrome due to a VIP-producing adrenal phaeochromocytoma.

P Quarles Van Ufford-Mannesse1, M Castro Cabezas, T M Vroom, A Van Gils, C J Lips, P Niermeijer.   

Abstract

A patient with neurofibromatosis type 1 and watery diarrhoea syndrome due to a VIP-producing adrenal phaeochromocytoma (Case Report). J Intern Med 1999; 246: 231-234. A 43-year-old patient with neurofibromatosis type 1 suffered from watery diarrhoea syndrome induced by excessive production of vasoactive intestinal polypeptide (VIP) in an adrenal phaeochromocytoma. This case report emphasizes that patients with neurofibromatosis are prone to develop more than one disease induced by tumours originating from the neural crest. Since excessive VIP production in a phaeochromocytoma may mask the symptoms of catecholamine overproduction, and in view of the therapeutic consequences, neurofibromatosis patients with hyperVIP-aemia must be checked for the presence of a phaeochromocytoma.

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Year:  1999        PMID： 10447793     DOI： 10.1046/j.1365-2796.1999.00533.x

Source DB:  PubMed          Journal:  J Intern Med        ISSN： 0954-6820            Impact factor:   8.989


  5 in total

Review 1.  Watery diarrhea, hypokalemia and achlorhydria syndrome due to an adrenal pheochromocytoma.

Authors:  Shin-ichi Ikuta; Chiaki Yasui; Masahiro Kawanaka; Tsukasa Aihara; Hidenori Yoshie; Hidenori Yanagi; Masao Mitsunobu; Ayako Sugihara; Naoki Yamanaka
Journal:  World J Gastroenterol       Date:  2007-09-14       Impact factor: 5.742

2.  Pheochromocytoma in von hippel-lindau disease: distinct histopathologic phenotype compared to pheochromocytoma in multiple endocrine neoplasia type 2.

Authors:  Christian A Koch; David Mauro; McClellan M Walther; W Marston Linehan; Alexander O Vortmeyer; Ronald Jaffe; Karel Pacak; George P Chrousos; Zhengping Zhuang; Irina A Lubensky
Journal:  Endocr Pathol       Date:  2002       Impact factor: 3.943

3.  Octreotide reverses shock due to vasoactive intestinal peptide-secreting adrenal pheochromocytoma: A case report and review of literature.

Authors:  Xiao Hu; Wei Cao; Min Zhao
Journal:  World J Clin Cases       Date:  2018-11-26       Impact factor: 1.337

4.  Case Report: Irreversible Watery Diarrhea, Severe Metabolic Acidosis, Hypokalemia and Achloridria Syndrome Related to Vasoactive Intestinal Peptide Secreting Malignant Pheochromocytoma.

Authors:  Aurelio Negro; Ignazio Verzicco; Stefano Tedeschi; Nicoletta Campanini; Magda Zanelli; Emanuele Negri; Enrico Farnetti; Davide Nicoli; Barbara Palladini; Rosaria Santi; Davide Cunzi; Anna Calvi; Pietro Coghi; Luigi Gerra; Riccardo Volpi; Gallia Graiani; Aderville Cabassi
Journal:  Front Endocrinol (Lausanne)       Date:  2021-03-17       Impact factor: 5.555

5.  A rare case of watery diarrhea, hypokalemia and achlorhydria syndrome caused by pheochromocytoma.

Authors:  Jingjing Jiang; Li Zhang; Zhaodi Wu; Zhilong Ai; Yingyong Hou; Zhiqiang Lu; Xin Gao
Journal:  BMC Cancer       Date:  2014-07-31       Impact factor: 4.430
  5 in total

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