| Literature DB >> 10408824 |
H J Bartz1, L Wiesner, F Wappler.
Abstract
Mucopolysaccharidosis IV, also known as Morquio-Brailsford syndrome, is an inherited autosomal recessive disorder of mucopolysaccharide metabolism leading to accumulation of keratan sulphate in the connective tissue of multiple organ systems. Based on a case report, the anaesthetic implications for the treatment of patients with MPS IV presenting for major orthopaedic surgery are discussed.Entities:
Mesh:
Year: 1999 PMID: 10408824 DOI: 10.1034/j.1399-6576.1999.430614.x
Source DB: PubMed Journal: Acta Anaesthesiol Scand ISSN: 0001-5172 Impact factor: 2.105