D H Perlmutter1. Show Affiliations » 1. Department of Pediatrics, Washington University School of Medicine, Children's Hospital, St. Louis, Missouri 63110, USA. Perlmutter@al.kids.wustl.edu
Abstract
Mesh: See more » AnimalsCystic Fibrosis/geneticsCystic Fibrosis/metabolismCystic Fibrosis Transmembrane Conductance Regulator/chemistryCystic Fibrosis Transmembrane Conductance Regulator/metabolismEndoplasmic Reticulum/metabolismGenetic Diseases, Inborn/metabolismHumansProtein FoldingProtein Processing, Post-Translationalalpha 1-Antitrypsin Deficiency/geneticsalpha 1-Antitrypsin Deficiency/metabolism
Substances: See more » CFTR protein, humanCystic Fibrosis Transmembrane Conductance Regulator
Year: 1999 PMID: 10378505
Source DB: PubMed Journal: Lab Invest ISSN: 0023-6837 Impact factor: 5.662