Literature DB >> 10341275

Prion protein conformation in a patient with sporadic fatal insomnia.

J A Mastrianni1, R Nixon, R Layzer, G C Telling, D Han, S J DeArmond, S B Prusiner.   

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Year:  1999        PMID： 10341275     DOI： 10.1056/NEJM199905273402104

Source DB:  PubMed          Journal:  N Engl J Med        ISSN： 0028-4793            Impact factor:   91.245


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  34 in total

1.  The [KIL-d] element specifically regulates viral gene expression in yeast.

Authors:  Z Tallóczy; R Mazar; D E Georgopoulos; F Ramos; M J Leibowitz
Journal:  Genetics       Date:  2000-06       Impact factor: 4.562

2.  Strain-specified relative conformational stability of the scrapie prion protein.

Authors:  D Peretz; M R Scott; D Groth; R A Williamson; D R Burton; F E Cohen; S B Prusiner
Journal:  Protein Sci       Date:  2001-04       Impact factor: 6.725

3.  Immunodetection of disease-associated mutant PrP, which accelerates disease in GSS transgenic mice.

Authors:  Karah E Nazor; Franziska Kuhn; Tanya Seward; Mike Green; Daniel Zwald; Mario Pürro; Jaqueline Schmid; Karin Biffiger; Aisling M Power; Bruno Oesch; Alex J Raeber; Glenn C Telling
Journal:  EMBO J       Date:  2005-06-16       Impact factor: 11.598

4.  Towards authentic transgenic mouse models of heritable PrP prion diseases.

Authors:  Joel C Watts; Kurt Giles; Matthew E C Bourkas; Smita Patel; Abby Oehler; Marta Gavidia; Sumita Bhardwaj; Joanne Lee; Stanley B Prusiner
Journal:  Acta Neuropathol       Date:  2016-06-28       Impact factor: 17.088

5.  An autopsy-verified case of FTLD-TDP type A with upper motor neuron-predominant motor neuron disease mimicking MM2-thalamic-type sporadic Creutzfeldt-Jakob disease.

Authors:  Yuichi Hayashi; Yasushi Iwasaki; Akira Takekoshi; Nobuaki Yoshikura; Takahiko Asano; Maya Mimuro; Akio Kimura; Katsuya Satoh; Tetsuyuki Kitamoto; Mari Yoshida; Takashi Inuzuka
Journal:  Prion       Date:  2016-11       Impact factor: 3.931

6.  Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene.

Authors:  Carsten Korth; Kiyotoshi Kaneko; Darlene Groth; Norbert Heye; Glenn Telling; James Mastrianni; Piero Parchi; Pierluigi Gambetti; Robert Will; James Ironside; Cornelia Heinrich; Patrick Tremblay; Stephen J DeArmond; Stanley B Prusiner
Journal:  Proc Natl Acad Sci U S A       Date:  2003-04-08       Impact factor: 11.205

7.  Requirements for mutant and wild-type prion protein misfolding in vitro.

Authors:  Geoffrey P Noble; Daniel J Walsh; Michael B Miller; Walker S Jackson; Surachai Supattapone
Journal:  Biochemistry       Date:  2015-01-22       Impact factor: 3.162

8.  A novel PRNP-P105S mutation associated with atypical prion disease and a rare PrPSc conformation.

Authors:  E Tunnell; R Wollman; S Mallik; C J Cortes; S J Dearmond; J A Mastrianni
Journal:  Neurology       Date:  2008-10-28       Impact factor: 9.910

9.  Live cell fluorescence resonance energy transfer predicts an altered molecular association of heterologous PrPSc with PrPC.

Authors:  Suparna Mallik; Wenbin Yang; Eric M Norstrom; James A Mastrianni
Journal:  J Biol Chem       Date:  2010-01-19       Impact factor: 5.157

10.  Clinical, histopathological and genetic studies in a case of fatal familial insomnia with review of the literature.

Authors:  Bin Peng; Shenqi Zhang; Hongjuan Dong; Zuneng Lu
Journal:  Int J Clin Exp Pathol       Date:  2015-09-01
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