Literature DB >> 10234616

Metabolic decompensation and lactic acidosis in propionic acidaemia complicated by thiamine deficiency.

E Mayatepek1, A Schulze.   

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Year:  1999        PMID: 10234616     DOI: 10.1023/a:1005418507365

Source DB:  PubMed          Journal:  J Inherit Metab Dis        ISSN: 0141-8955            Impact factor:   4.982


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  2 in total

1.  Primary treatment of propionic acidemia complicated by acute thiamine deficiency.

Authors:  D Matern; H H Seydewitz; W Lehnert; H Niederhoff; J U Leititis; M Brandis
Journal:  J Pediatr       Date:  1996-11       Impact factor: 4.406

2.  Studies on the effects of saturated and unsaturated short-chain monocarboxylic acids on the energy metabolism of rat liver mitochondria.

Authors:  N Gregersen
Journal:  Pediatr Res       Date:  1979-11       Impact factor: 3.756

  2 in total
  2 in total

1.  Wernicke-like encephalopathy during classic maple syrup urine disease decompensation.

Authors:  R Manara; M Del Rizzo; A P Burlina; A Bordugo; V Citton; P Rodriguez-Pombo; M Ugarte; A B Burlina
Journal:  J Inherit Metab Dis       Date:  2012-02-18       Impact factor: 4.982

Review 2.  Emergency management of inherited metabolic diseases.

Authors:  V Prietsch; M Lindner; J Zschocke; W L Nyhan; G F Hoffmann
Journal:  J Inherit Metab Dis       Date:  2002-11       Impact factor: 4.982

  2 in total

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