Literature DB >> 10021451

Novel pharmacologic therapies for cystic fibrosis.

P L Zeitlin1.   

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Year:  1999        PMID： 10021451      PMCID： PMC408112          DOI： 10.1172/JCI6346

Source DB:  PubMed          Journal:  J Clin Invest        ISSN： 0021-9738            Impact factor:   14.808


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  43 in total

1.  Correcting temperature-sensitive protein folding defects.

Authors:  C R Brown; L Q Hong-Brown; W J Welch
Journal:  J Clin Invest       Date:  1997-03-15       Impact factor: 14.808

2.  8-cyclopentyl-1,3-dipropylxanthine and other xanthines differentially bind to the wild-type and delta F508 first nucleotide binding fold (NBF-1) domains of the cystic fibrosis transmembrane conductance regulator.

Authors:  B E Cohen; G Lee; K A Jacobson; Y C Kim; Z Huang; E J Sorscher; H B Pollard
Journal:  Biochemistry       Date:  1997-05-27       Impact factor: 3.162

3.  Delta F508-CFTR channels: kinetics, activation by forskolin, and potentiation by xanthines.

Authors:  C M Haws; I B Nepomuceno; M E Krouse; H Wakelee; T Law; Y Xia; H Nguyen; J J Wine
Journal:  Am J Physiol       Date:  1996-05

4.  Direct action of genistein on CFTR.

Authors:  F Weinreich; P G Wood; J R Riordan; G Nagel
Journal:  Pflugers Arch       Date:  1997-08       Impact factor: 3.657

5.  Multiple proteolytic systems, including the proteasome, contribute to CFTR processing.

Authors:  T J Jensen; M A Loo; S Pind; D B Williams; A L Goldberg; J R Riordan
Journal:  Cell       Date:  1995-10-06       Impact factor: 41.582

Review 6.  Genetic disorders of membrane transport. II. Regulation of CFTR by small molecules including HCO3-.

Authors:  B Illek; H Fischer; T E Machen
Journal:  Am J Physiol       Date:  1998-12

7.  Aminoglycoside antibiotics restore CFTR function by overcoming premature stop mutations.

Authors:  M Howard; R A Frizzell; D M Bedwell
Journal:  Nat Med       Date:  1996-04       Impact factor: 53.440

8.  Phosphorylation-dependent block of cystic fibrosis transmembrane conductance regulator chloride channel by exogenous R domain protein.

Authors:  J Ma; J E Tasch; T Tao; J Zhao; J Xie; M L Drumm; P B Davis
Journal:  J Biol Chem       Date:  1996-03-29       Impact factor: 5.157

9.  Regulation of epithelial sodium channels by the cystic fibrosis transmembrane conductance regulator.

Authors:  I I Ismailov; M S Awayda; B Jovov; B K Berdiev; C M Fuller; J R Dedman; M Kaetzel; D J Benos
Journal:  J Biol Chem       Date:  1996-03-01       Impact factor: 5.157

10.  Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid.

Authors:  J J Smith; S M Travis; E P Greenberg; M J Welsh
Journal:  Cell       Date:  1996-04-19       Impact factor: 41.582
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  9 in total

Review 1.  Atypical cystic fibrosis--diagnostic and management dilemmas.

Authors:  Colin Wallis
Journal:  J R Soc Med       Date:  2003       Impact factor: 5.344

2.  Sildenafil (Viagra) corrects DeltaF508-CFTR location in nasal epithelial cells from patients with cystic fibrosis.

Authors:  R L Dormer; C M Harris; Z Clark; M M C Pereira; I J M Doull; C Norez; F Becq; M A McPherson
Journal:  Thorax       Date:  2005-01       Impact factor: 9.139

3.  The iodide-transport-defect-causing mutation R124H: a δ-amino group at position 124 is critical for maturation and trafficking of the Na+/I- symporter.

Authors:  Viktoriya Paroder; Juan P Nicola; Christopher S Ginter; Nancy Carrasco
Journal:  J Cell Sci       Date:  2013-05-20       Impact factor: 5.285

4.  Interference with ubiquitination in CFTR modifies stability of core glycosylated and cell surface pools.

Authors:  Seakwoo Lee; Mark J Henderson; Eric Schiffhauer; Jordan Despanie; Katherine Henry; Po Wei Kang; Douglas Walker; Michelle L McClure; Landon Wilson; Eric J Sorscher; Pamela L Zeitlin
Journal:  Mol Cell Biol       Date:  2014-07       Impact factor: 4.272

Review 5.  Targeted therapy for cystic fibrosis: cystic fibrosis transmembrane conductance regulator mutation-specific pharmacologic strategies.

Authors:  Ronald C Rubenstein
Journal:  Mol Diagn Ther       Date:  2006       Impact factor: 4.074

Review 6.  Applications of proteomic technologies for understanding the premature proteolysis of CFTR.

Authors:  Mark J Henderson; Om V Singh; Pamela L Zeitlin
Journal:  Expert Rev Proteomics       Date:  2010-08       Impact factor: 3.940

Review 7.  Recent advances in cystic fibrosis.

Authors:  I J Doull
Journal:  Arch Dis Child       Date:  2001-07       Impact factor: 3.791

Review 8.  Diagnosis of cystic fibrosis.

Authors:  Karen Z Voter; Clement L Ren
Journal:  Clin Rev Allergy Immunol       Date:  2008-12       Impact factor: 8.667

Review 9.  Transcriptomic and Proteostasis Networks of CFTR and the Development of Small Molecule Modulators for the Treatment of Cystic Fibrosis Lung Disease.

Authors:  Matthew D Strub; Paul B McCray
Journal:  Genes (Basel)       Date:  2020-05-13       Impact factor: 4.096
  9 in total

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